Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome

Autores
Baenas, Diego Federico; Flores Balverdi, Janet; Retamozo, Maria Soledad; Riscanevo, Nadia; Alvarez, Cecilia Susana; De la Fuente, Jorge; Caeiro, Francisco
Año de publicación
2018
Idioma
español castellano
Tipo de recurso
artículo
Estado
versión publicada
Descripción
Primary Sjögren´s syndrome is a systemic and chronic autoimmune disease. Renal involvement may occur in up to 30% of patients. The incidence of tubulopathies ranges from 2.6 to 33%. They are manifested by defects in the urine concentration and hydroelectrolyte alterations, mainly distal tubular acidosis and exceptionally proximal tubular acidosis. These disorders can be associated with nephrocalcinosis and renal lithiasis. We report the case of a patient with primary Sjögren who presented proximal renal tubular acidosis associated with recurrent renal colic due to renal lithiasis and nephrocalcinosis. We highlight the importance of diagnosing renal tubular acidosis in patients with Sjögren´s syndrome that present alterations in urinary sediment and electrolyte disorders to avoid nephrocalcinosis and nephrolithiasis. Acidosis correction treatment aims to prevent the progression of the disorder and preserve renal function.
Fil: Baenas, Diego Federico. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Flores Balverdi, Janet. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Retamozo, Maria Soledad. Hospital Privado Centro Medico de Córdoba; Argentina. Consejo Nacional de Investigaciones Científicas y Técnicas. Centro Científico Tecnológico Conicet - Córdoba. Instituto de Investigaciones en Ciencias de la Salud. Universidad Nacional de Córdoba. Instituto de Investigaciones en Ciencias de la Salud; Argentina
Fil: Riscanevo, Nadia. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Alvarez, Cecilia Susana. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: De la Fuente, Jorge. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Caeiro, Francisco. Hospital Privado Centro Medico de Córdoba; Argentina
Materia
NEPHROCALCINOSIS
RENAL TUBULAR ACIDOSIS
PRIMARY SJOGREN'S SYNDROME
Nivel de accesibilidad
acceso abierto
Condiciones de uso
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
Repositorio
CONICET Digital (CONICET)
Institución
Consejo Nacional de Investigaciones Científicas y Técnicas
OAI Identificador
oai:ri.conicet.gov.ar:11336/92350

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spelling Nephrocalcinosis and proximal tubulopathy in Sjögren's SyndromeBaenas, Diego FedericoFlores Balverdi, JanetRetamozo, Maria SoledadRiscanevo, NadiaAlvarez, Cecilia SusanaDe la Fuente, JorgeCaeiro, FranciscoNEPHROCALCINOSISRENAL TUBULAR ACIDOSISPRIMARY SJOGREN'S SYNDROMEhttps://purl.org/becyt/ford/3.2https://purl.org/becyt/ford/3Primary Sjögren´s syndrome is a systemic and chronic autoimmune disease. Renal involvement may occur in up to 30% of patients. The incidence of tubulopathies ranges from 2.6 to 33%. They are manifested by defects in the urine concentration and hydroelectrolyte alterations, mainly distal tubular acidosis and exceptionally proximal tubular acidosis. These disorders can be associated with nephrocalcinosis and renal lithiasis. We report the case of a patient with primary Sjögren who presented proximal renal tubular acidosis associated with recurrent renal colic due to renal lithiasis and nephrocalcinosis. We highlight the importance of diagnosing renal tubular acidosis in patients with Sjögren´s syndrome that present alterations in urinary sediment and electrolyte disorders to avoid nephrocalcinosis and nephrolithiasis. Acidosis correction treatment aims to prevent the progression of the disorder and preserve renal function.Fil: Baenas, Diego Federico. Hospital Privado Centro Medico de Córdoba; ArgentinaFil: Flores Balverdi, Janet. Hospital Privado Centro Medico de Córdoba; ArgentinaFil: Retamozo, Maria Soledad. Hospital Privado Centro Medico de Córdoba; Argentina. Consejo Nacional de Investigaciones Científicas y Técnicas. Centro Científico Tecnológico Conicet - Córdoba. Instituto de Investigaciones en Ciencias de la Salud. Universidad Nacional de Córdoba. Instituto de Investigaciones en Ciencias de la Salud; ArgentinaFil: Riscanevo, Nadia. Hospital Privado Centro Medico de Córdoba; ArgentinaFil: Alvarez, Cecilia Susana. Hospital Privado Centro Medico de Córdoba; ArgentinaFil: De la Fuente, Jorge. Hospital Privado Centro Medico de Córdoba; ArgentinaFil: Caeiro, Francisco. Hospital Privado Centro Medico de Córdoba; ArgentinaUniversidad Nacional de Córdoba2018-06info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionhttp://purl.org/coar/resource_type/c_6501info:ar-repo/semantics/articuloapplication/pdfapplication/pdfhttp://hdl.handle.net/11336/92350Baenas, Diego Federico; Flores Balverdi, Janet; Retamozo, Maria Soledad; Riscanevo, Nadia; Alvarez, Cecilia Susana; et al.; Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome; Universidad Nacional de Córdoba; Revista de la Facultad de Ciencias Médicas; 75; 2; 6-2018; 138-1420014-67221853-0605CONICET DigitalCONICETspainfo:eu-repo/semantics/altIdentifier/url/https://revistas.unc.edu.ar/index.php/med/article/view/19161info:eu-repo/semantics/altIdentifier/doi/10.31053/1853.0605.v75.n2.19161info:eu-repo/semantics/altIdentifier/url/https://www.ncbi.nlm.nih.gov/pubmed/30273538info:eu-repo/semantics/openAccesshttps://creativecommons.org/licenses/by-nc-sa/2.5/ar/reponame:CONICET Digital (CONICET)instname:Consejo Nacional de Investigaciones Científicas y Técnicas2025-09-03T10:01:59Zoai:ri.conicet.gov.ar:11336/92350instacron:CONICETInstitucionalhttp://ri.conicet.gov.ar/Organismo científico-tecnológicoNo correspondehttp://ri.conicet.gov.ar/oai/requestdasensio@conicet.gov.ar; lcarlino@conicet.gov.arArgentinaNo correspondeNo correspondeNo correspondeopendoar:34982025-09-03 10:01:59.7CONICET Digital (CONICET) - Consejo Nacional de Investigaciones Científicas y Técnicasfalse
dc.title.none.fl_str_mv Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
title Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
spellingShingle Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
Baenas, Diego Federico
NEPHROCALCINOSIS
RENAL TUBULAR ACIDOSIS
PRIMARY SJOGREN'S SYNDROME
title_short Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
title_full Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
title_fullStr Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
title_full_unstemmed Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
title_sort Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome
dc.creator.none.fl_str_mv Baenas, Diego Federico
Flores Balverdi, Janet
Retamozo, Maria Soledad
Riscanevo, Nadia
Alvarez, Cecilia Susana
De la Fuente, Jorge
Caeiro, Francisco
author Baenas, Diego Federico
author_facet Baenas, Diego Federico
Flores Balverdi, Janet
Retamozo, Maria Soledad
Riscanevo, Nadia
Alvarez, Cecilia Susana
De la Fuente, Jorge
Caeiro, Francisco
author_role author
author2 Flores Balverdi, Janet
Retamozo, Maria Soledad
Riscanevo, Nadia
Alvarez, Cecilia Susana
De la Fuente, Jorge
Caeiro, Francisco
author2_role author
author
author
author
author
author
dc.subject.none.fl_str_mv NEPHROCALCINOSIS
RENAL TUBULAR ACIDOSIS
PRIMARY SJOGREN'S SYNDROME
topic NEPHROCALCINOSIS
RENAL TUBULAR ACIDOSIS
PRIMARY SJOGREN'S SYNDROME
purl_subject.fl_str_mv https://purl.org/becyt/ford/3.2
https://purl.org/becyt/ford/3
dc.description.none.fl_txt_mv Primary Sjögren´s syndrome is a systemic and chronic autoimmune disease. Renal involvement may occur in up to 30% of patients. The incidence of tubulopathies ranges from 2.6 to 33%. They are manifested by defects in the urine concentration and hydroelectrolyte alterations, mainly distal tubular acidosis and exceptionally proximal tubular acidosis. These disorders can be associated with nephrocalcinosis and renal lithiasis. We report the case of a patient with primary Sjögren who presented proximal renal tubular acidosis associated with recurrent renal colic due to renal lithiasis and nephrocalcinosis. We highlight the importance of diagnosing renal tubular acidosis in patients with Sjögren´s syndrome that present alterations in urinary sediment and electrolyte disorders to avoid nephrocalcinosis and nephrolithiasis. Acidosis correction treatment aims to prevent the progression of the disorder and preserve renal function.
Fil: Baenas, Diego Federico. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Flores Balverdi, Janet. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Retamozo, Maria Soledad. Hospital Privado Centro Medico de Córdoba; Argentina. Consejo Nacional de Investigaciones Científicas y Técnicas. Centro Científico Tecnológico Conicet - Córdoba. Instituto de Investigaciones en Ciencias de la Salud. Universidad Nacional de Córdoba. Instituto de Investigaciones en Ciencias de la Salud; Argentina
Fil: Riscanevo, Nadia. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Alvarez, Cecilia Susana. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: De la Fuente, Jorge. Hospital Privado Centro Medico de Córdoba; Argentina
Fil: Caeiro, Francisco. Hospital Privado Centro Medico de Córdoba; Argentina
description Primary Sjögren´s syndrome is a systemic and chronic autoimmune disease. Renal involvement may occur in up to 30% of patients. The incidence of tubulopathies ranges from 2.6 to 33%. They are manifested by defects in the urine concentration and hydroelectrolyte alterations, mainly distal tubular acidosis and exceptionally proximal tubular acidosis. These disorders can be associated with nephrocalcinosis and renal lithiasis. We report the case of a patient with primary Sjögren who presented proximal renal tubular acidosis associated with recurrent renal colic due to renal lithiasis and nephrocalcinosis. We highlight the importance of diagnosing renal tubular acidosis in patients with Sjögren´s syndrome that present alterations in urinary sediment and electrolyte disorders to avoid nephrocalcinosis and nephrolithiasis. Acidosis correction treatment aims to prevent the progression of the disorder and preserve renal function.
publishDate 2018
dc.date.none.fl_str_mv 2018-06
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
http://purl.org/coar/resource_type/c_6501
info:ar-repo/semantics/articulo
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv http://hdl.handle.net/11336/92350
Baenas, Diego Federico; Flores Balverdi, Janet; Retamozo, Maria Soledad; Riscanevo, Nadia; Alvarez, Cecilia Susana; et al.; Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome; Universidad Nacional de Córdoba; Revista de la Facultad de Ciencias Médicas; 75; 2; 6-2018; 138-142
0014-6722
1853-0605
CONICET Digital
CONICET
url http://hdl.handle.net/11336/92350
identifier_str_mv Baenas, Diego Federico; Flores Balverdi, Janet; Retamozo, Maria Soledad; Riscanevo, Nadia; Alvarez, Cecilia Susana; et al.; Nephrocalcinosis and proximal tubulopathy in Sjögren's Syndrome; Universidad Nacional de Córdoba; Revista de la Facultad de Ciencias Médicas; 75; 2; 6-2018; 138-142
0014-6722
1853-0605
CONICET Digital
CONICET
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv info:eu-repo/semantics/altIdentifier/url/https://revistas.unc.edu.ar/index.php/med/article/view/19161
info:eu-repo/semantics/altIdentifier/doi/10.31053/1853.0605.v75.n2.19161
info:eu-repo/semantics/altIdentifier/url/https://www.ncbi.nlm.nih.gov/pubmed/30273538
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
eu_rights_str_mv openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv Universidad Nacional de Córdoba
publisher.none.fl_str_mv Universidad Nacional de Córdoba
dc.source.none.fl_str_mv reponame:CONICET Digital (CONICET)
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instname_str Consejo Nacional de Investigaciones Científicas y Técnicas
repository.name.fl_str_mv CONICET Digital (CONICET) - Consejo Nacional de Investigaciones Científicas y Técnicas
repository.mail.fl_str_mv dasensio@conicet.gov.ar; lcarlino@conicet.gov.ar
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