Malignant extra-adrenal pelvic paraganglioma in a paediatric patient

Autores
Cao, Gabriel Fernando; Mendez, Julian; Navacchia, Daniel
Año de publicación
2017
Idioma
inglés
Tipo de recurso
artículo
Estado
versión publicada
Descripción
The extra-adrenal paraganglioma is a neoplasm originating in regional structures, uncommon in paediatrics. We report on a case of a 13-year-old patient who began with severe arterial hypertension, tachycardia, dilated cardiomyopathy and elevated levels of catecholamines in the blood and urine. The presence of a retrovesical pelvic mass in contact with the right vaginal dome was determined by imaging studies. A diagnosis of malignant extra-adrenal pelvic paraganglioma with lymph node metastases was reached through biopsy and the surgical resection of subsequent local recurrences. Paragangliomas are usually located in the paravertebral zones from the base of the skull to the retroperitoneum and are benign in 90% of cases. This kind of neoplasia is uncommon in paediatrics, especially those located in the pelvis. In cases of masses of a gynaecological origin, a differential diagnosis should be considered, and a histological and immunohistochemical study is essential in certifying the diagnosis.
Fil: Cao, Gabriel Fernando. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
Fil: Mendez, Julian. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
Fil: Navacchia, Daniel. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
Materia
EXTRA-ADRENAL
MALIGNANCY
PAEDIATRICS
PARAGANGLIOMA
Nivel de accesibilidad
acceso abierto
Condiciones de uso
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
Repositorio
CONICET Digital (CONICET)
Institución
Consejo Nacional de Investigaciones Científicas y Técnicas
OAI Identificador
oai:ri.conicet.gov.ar:11336/66451
Acceder
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network_acronym_str CONICETDig
repository_id_str 3498
network_name_str CONICET Digital (CONICET)
spelling Malignant extra-adrenal pelvic paraganglioma in a paediatric patientCao, Gabriel FernandoMendez, JulianNavacchia, DanielEXTRA-ADRENALMALIGNANCYPAEDIATRICSPARAGANGLIOMAhttps://purl.org/becyt/ford/3.1https://purl.org/becyt/ford/3The extra-adrenal paraganglioma is a neoplasm originating in regional structures, uncommon in paediatrics. We report on a case of a 13-year-old patient who began with severe arterial hypertension, tachycardia, dilated cardiomyopathy and elevated levels of catecholamines in the blood and urine. The presence of a retrovesical pelvic mass in contact with the right vaginal dome was determined by imaging studies. A diagnosis of malignant extra-adrenal pelvic paraganglioma with lymph node metastases was reached through biopsy and the surgical resection of subsequent local recurrences. Paragangliomas are usually located in the paravertebral zones from the base of the skull to the retroperitoneum and are benign in 90% of cases. This kind of neoplasia is uncommon in paediatrics, especially those located in the pelvis. In cases of masses of a gynaecological origin, a differential diagnosis should be considered, and a histological and immunohistochemical study is essential in certifying the diagnosis.Fil: Cao, Gabriel Fernando. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); ArgentinaFil: Mendez, Julian. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); ArgentinaFil: Navacchia, Daniel. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); ArgentinaCancer Intelligence2017-08info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionhttp://purl.org/coar/resource_type/c_6501info:ar-repo/semantics/articuloapplication/pdfapplication/pdfhttp://hdl.handle.net/11336/66451Cao, Gabriel Fernando; Mendez, Julian; Navacchia, Daniel; Malignant extra-adrenal pelvic paraganglioma in a paediatric patient; Cancer Intelligence; Ccancermedicalscience; 11; 8-20171754-6605CONICET DigitalCONICETenginfo:eu-repo/semantics/altIdentifier/doi/10.3332/ecancer.2017.761info:eu-repo/semantics/altIdentifier/url/https://ecancer.org/journal/11/full/761-malignant-extra-adrenal-pelvic-paraganglioma-in-a-paediatric-patient.phpinfo:eu-repo/semantics/openAccesshttps://creativecommons.org/licenses/by-nc-sa/2.5/ar/reponame:CONICET Digital (CONICET)instname:Consejo Nacional de Investigaciones Científicas y Técnicas2025-09-29T09:54:02Zoai:ri.conicet.gov.ar:11336/66451instacron:CONICETInstitucionalhttp://ri.conicet.gov.ar/Organismo científico-tecnológicoNo correspondehttp://ri.conicet.gov.ar/oai/requestdasensio@conicet.gov.ar; lcarlino@conicet.gov.arArgentinaNo correspondeNo correspondeNo correspondeopendoar:34982025-09-29 09:54:02.648CONICET Digital (CONICET) - Consejo Nacional de Investigaciones Científicas y Técnicasfalse
dc.title.none.fl_str_mv Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
title Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
spellingShingle Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
Cao, Gabriel Fernando
EXTRA-ADRENAL
MALIGNANCY
PAEDIATRICS
PARAGANGLIOMA
title_short Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
title_full Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
title_fullStr Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
title_full_unstemmed Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
title_sort Malignant extra-adrenal pelvic paraganglioma in a paediatric patient
dc.creator.none.fl_str_mv Cao, Gabriel Fernando
Mendez, Julian
Navacchia, Daniel
author Cao, Gabriel Fernando
author_facet Cao, Gabriel Fernando
Mendez, Julian
Navacchia, Daniel
author_role author
author2 Mendez, Julian
Navacchia, Daniel
author2_role author
author
dc.subject.none.fl_str_mv EXTRA-ADRENAL
MALIGNANCY
PAEDIATRICS
PARAGANGLIOMA
topic EXTRA-ADRENAL
MALIGNANCY
PAEDIATRICS
PARAGANGLIOMA
purl_subject.fl_str_mv https://purl.org/becyt/ford/3.1
https://purl.org/becyt/ford/3
dc.description.none.fl_txt_mv The extra-adrenal paraganglioma is a neoplasm originating in regional structures, uncommon in paediatrics. We report on a case of a 13-year-old patient who began with severe arterial hypertension, tachycardia, dilated cardiomyopathy and elevated levels of catecholamines in the blood and urine. The presence of a retrovesical pelvic mass in contact with the right vaginal dome was determined by imaging studies. A diagnosis of malignant extra-adrenal pelvic paraganglioma with lymph node metastases was reached through biopsy and the surgical resection of subsequent local recurrences. Paragangliomas are usually located in the paravertebral zones from the base of the skull to the retroperitoneum and are benign in 90% of cases. This kind of neoplasia is uncommon in paediatrics, especially those located in the pelvis. In cases of masses of a gynaecological origin, a differential diagnosis should be considered, and a histological and immunohistochemical study is essential in certifying the diagnosis.
Fil: Cao, Gabriel Fernando. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
Fil: Mendez, Julian. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
Fil: Navacchia, Daniel. Gobierno de la Ciudad de Buenos Aires. Hospital General de Niños Pedro Elizalde (ex Casa Cuna); Argentina
description The extra-adrenal paraganglioma is a neoplasm originating in regional structures, uncommon in paediatrics. We report on a case of a 13-year-old patient who began with severe arterial hypertension, tachycardia, dilated cardiomyopathy and elevated levels of catecholamines in the blood and urine. The presence of a retrovesical pelvic mass in contact with the right vaginal dome was determined by imaging studies. A diagnosis of malignant extra-adrenal pelvic paraganglioma with lymph node metastases was reached through biopsy and the surgical resection of subsequent local recurrences. Paragangliomas are usually located in the paravertebral zones from the base of the skull to the retroperitoneum and are benign in 90% of cases. This kind of neoplasia is uncommon in paediatrics, especially those located in the pelvis. In cases of masses of a gynaecological origin, a differential diagnosis should be considered, and a histological and immunohistochemical study is essential in certifying the diagnosis.
publishDate 2017
dc.date.none.fl_str_mv 2017-08
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
http://purl.org/coar/resource_type/c_6501
info:ar-repo/semantics/articulo
format article
status_str publishedVersion
dc.identifier.none.fl_str_mv http://hdl.handle.net/11336/66451
Cao, Gabriel Fernando; Mendez, Julian; Navacchia, Daniel; Malignant extra-adrenal pelvic paraganglioma in a paediatric patient; Cancer Intelligence; Ccancermedicalscience; 11; 8-2017
1754-6605
CONICET Digital
CONICET
url http://hdl.handle.net/11336/66451
identifier_str_mv Cao, Gabriel Fernando; Mendez, Julian; Navacchia, Daniel; Malignant extra-adrenal pelvic paraganglioma in a paediatric patient; Cancer Intelligence; Ccancermedicalscience; 11; 8-2017
1754-6605
CONICET Digital
CONICET
dc.language.none.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv info:eu-repo/semantics/altIdentifier/doi/10.3332/ecancer.2017.761
info:eu-repo/semantics/altIdentifier/url/https://ecancer.org/journal/11/full/761-malignant-extra-adrenal-pelvic-paraganglioma-in-a-paediatric-patient.php
dc.rights.none.fl_str_mv info:eu-repo/semantics/openAccess
https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
eu_rights_str_mv openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by-nc-sa/2.5/ar/
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv Cancer Intelligence
publisher.none.fl_str_mv Cancer Intelligence
dc.source.none.fl_str_mv reponame:CONICET Digital (CONICET)
instname:Consejo Nacional de Investigaciones Científicas y Técnicas
reponame_str CONICET Digital (CONICET)
collection CONICET Digital (CONICET)
instname_str Consejo Nacional de Investigaciones Científicas y Técnicas
repository.name.fl_str_mv CONICET Digital (CONICET) - Consejo Nacional de Investigaciones Científicas y Técnicas
repository.mail.fl_str_mv dasensio@conicet.gov.ar; lcarlino@conicet.gov.ar
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score 13.070432

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